Tetralogía de Fallot con agenesia de válvula pulmonar en el recién nacido y lactante. Corrección completa
- A. Cabrera Duro
- D. Rodrigo Carbonero
- P. Martínez Corrales
- J. Aramendi Gallardo
- J. Alcíbar Villa
- J. López de Heredia Goya
- C. Romero Ibarra
ISSN: 1695-4033, 1696-4608
Year of publication: 2004
Volume: 60
Issue: 2
Pages: 180-183
Type: Article
More publications in: Anales de Pediatría: Publicación Oficial de la Asociación Española de Pediatría ( AEP )
Abstract
Creemos que el tratamiento precoz evita la degeneración de la vóa respiratoria y la sobrecarga de volumen del ventróculo derecho We report two patients, a newborn and a 7-month old infant, with tetralogy of Fallot and absent pulmonary valve syndrome. Both had severe obstruction at the level of the ring with aneurysmal pulmonary artery branches, which compressed and displaced the trachea and main bronchial tubes. The neonate required mechanical ventilation from birth. Treatment was aggressive in both patients with interventricular septum defect closure, arterioplasty of the branches and homograft in the infant, and resection of the truncus and pulmonary branches with posterior face suture of both branches associated with a valved conduit in orthotopic position in the neonate We believe that early treatment avoids airway degeneration and right ventricle volume overload