Recomendaciones nutricionales para pacientes con seudohipoparatiroidismo
- Lorena Miñones-Suarez
- Guiomar Pérez de Nanclares
- Silvia Marín-del Barrio
- María José Alcázar Villar
- Diego de Sotto-Esteban
- Eduard Mogas
- Lourdes Rey Cordo
- Isolina Riaño-Galán
- Javier Lumbreras Fernández
- Rosaura Leis
ISSN: 1695-4033, 1696-4608
Ano de publicación: 2023
Volume: 99
Número: 2
Páxinas: 129-135
Tipo: Artigo
Outras publicacións en: Anales de Pediatría: Publicación Oficial de la Asociación Española de Pediatría ( AEP )
Resumo
Pseudohypoparathyroidism (PHP) is a spectrum of diseases characterized by insensitivity of target tissues to the action of parathyroid hormone and, consequently, by the presence of hyperphosphatemia and hypocalcaemia of varying severity. Early-onset obesity is a feature of PHP type 1A. This article discusses the need to establish uniform criteria to guide the nutritional management of patients with PHP. A decrease in energy expenditure calls for an adjustment of the energy content of the diet. Reducing the intake of foods rich in inorganic phosphorus helps manage hyperphosphataemia. Targeted nutrition should be part of the treatment plan of children and adolescents with PHP, since it contributes to modulating the calcium and phosphorus metabolism imbalances characteristic of these patients.